|
| ANCA-associated vasculitides (AAV) |
|
| Microscopic polyangiitis (MPA) | Chapel Hill Consensus Conference nomenclature [23] |
| Wegener’s granulomatosis (WG) | ACR Classification Criteria for WG [24] |
| Churg-Strauss syndrome (CSS) | ACR Classification Criteria for CSS [25] |
|
| Other vasculitides |
|
| Polyarteritis nodosa (PAN) | ACR Classification Criteria for PAN [26] |
| Behçet’s disease (BD) | International Criteria for BD [27] |
| Henoch-Schönlein purpura (HSP) | ACR Classification Criteria for HSP [28] |
| Cryoglobulinemic vasculitis | Chapel Hill Consensus Conference nomenclature [23] |
| Secondary vasculitis | Diagnostic criteria of underlying disease, histological confirmation |
| Undefined vasculitis | Clinical features without histological confirmation |
|
| Gastrointestinal disorders (GD) |
|
| Inflammatory bowel disease (IBD) | Clinical, endoscopic, radiological and histological criteria [29] |
| Primary sclerosing cholangitis | Clinical, radiological and immunological criteria [30] |
| Autoimmune hepatitis (AIH) | International Criteria for AIH [31] |
| Primary biliary cirrhosis | Clinical, biochemical, immunological and histological criteria [32] |
|
| Connective tissue diseases (CTD) |
|
| Systemic lupus erythematosus (SLE) | Updated revised ACR Criteria for SLE [33] |
| Rheumatoid arthritis (RA) | Revised ARA criteria for RA [34] |
| Felty’s syndrome | Clinical, radiological and laboratory criteria [35] |
| Systemic sclerosis (SSc) | ARA preliminary classification Criteria for SSc [36] |
| Dermatomyositis (DM) | Bohan and Peter diagnostic Criteria for DM [37, 38] |
| Sjögren’s syndrome (SjS) | Revised International Classification Criteria for SjS [39] |
| Mixed connective tissue disease (MCTD) | Alarcon-Segovia Diagnostic Criteria for MCTD [40] |
| Reiter’s syndrome | Clinical, radiological and immunological criteria [41] |
| Ankylosing spondylitis | Clinical, radiological and immunological criteria [42] |
| Juvenile chronic arthritis | Clinical, radiological and immunological criteria [43] |
| Relapsing polychondritis | Clinical, radiological and histological criteria [44] |
| Psoriasis | Clinical features |
| Antiphospholipid syndrome | Clinical and laboratory criteria [45] |
| Rheumatic polymyalgia | Clinical features and laboratory findings |
|
| Infections |
|
| Tuberculosis (TBC) | |
| S. aureus (subacute endocarditis) | |
| Other bacterial infections | Clinical features and laboratory findings |
| AIDS |
| Hepatitis C | |
| Aspergillosis | |
|
| Renal diseases (RD) |
|
| Poststreptococcal nephropathy (PSGN) | |
| IgA nephropathy | Laboratory and immunological findings, histological confirmation |
| Goodpasture’s disease |
| Membranous nephropathy | |
|
| Malignancies |
|
| Carcinoma | |
| Lymphoma | Clinical features, laboratory findings, histological confirmation |
| Chronic myelocytic leukaemia |
| Myelodysplasia |
| Monoclonal gammopathies | |
| Neurological disorders (ND) |
|
Demyelinating disease Stroke | Neurological symptoms and imaging findings |
|
| Miscellaneous disorders |
|
| Sarcoidosis | Clinical features, laboratory and imaging findings |
| Autoimmune hemolytic anemia (AHA) | Clinical features and laboratory findings |
| Pulmonary fibrosis | Imaging findings, histological confirmation |
|
| Medication |
|
| Antithyroid drugs | |
| Allopurinol | History of medication treatment |
| Phenytoin | |
|