Review Article
Neurological Disorders in Primary Sjögren's Syndrome
Table 1
Neurological manifestations in primary Sjögren’s syndrome.
| Peripheral disorders | Central disorders |
| Axonal polyneuropathies (i) Symmetric pure sensory peripheral neuropathy (ii) Symmetric sensorimotor peripheral neuropathy | Focal (i) Seizures (ii) Movement disorders (iii) Cerebellar syndrome (iv) Optic neuropathies (v) Pseudotumor lesions (vi) Motor and sensory loss
|
| Sensory ganglioneuronopathy | Multifocal disease (i) Cognitive impairment (ii) Encephalopathy (iii) Dementia (iv) Psychiatric abnormalities (v) Aseptic meningoencephalitis
|
| Motor neuropathy | Spinal cord dysfunction (i) Chronic progressive myelopathy (ii) Lower motor neuron disease (iii) Neurogenic bladder (iv) Acute transverse myelitis
|
| Small-fiber neuropathy | Progressive-multiple sclerosis-like syndrome |
| Multiple mononeuritis | Central nervous system vasculitic involvement |
| Trigeminal and other cranial nerves neuropathies | |
| Autonomic neuropathies | |
| Demyelinating polyradiculoneuropathy | |
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