Review Article

Neurological Disorders in Primary Sjögren's Syndrome

Table 1

Neurological manifestations in primary Sjögren’s syndrome.

Peripheral disordersCentral disorders

Axonal polyneuropathies
 (i) Symmetric pure sensory peripheral neuropathy
 (ii) Symmetric sensorimotor peripheral neuropathy
Focal
  (i) Seizures
  (ii) Movement disorders
  (iii) Cerebellar syndrome
  (iv) Optic neuropathies
  (v) Pseudotumor lesions
  (vi) Motor and sensory loss

Sensory ganglioneuronopathyMultifocal disease
  (i) Cognitive impairment
  (ii) Encephalopathy
  (iii) Dementia
  (iv) Psychiatric abnormalities
  (v) Aseptic meningoencephalitis

Motor neuropathySpinal cord dysfunction
  (i) Chronic progressive   myelopathy
  (ii) Lower motor neuron disease
  (iii) Neurogenic bladder
  (iv) Acute transverse myelitis

Small-fiber neuropathyProgressive-multiple sclerosis-like syndrome

Multiple mononeuritisCentral nervous system vasculitic involvement

Trigeminal and other cranial nerves neuropathies

Autonomic neuropathies

Demyelinating polyradiculoneuropathy