Review Article

Peripheral T-Cell Lymphoma: Review and Updates of Current Management Strategies

Table 1

List of T-cell lymphomas adapted from the 2008 WHO classification of mature T-cell and NK-cell Neoplasms.

Cutaneous
(i) Mycosis fungoides
(ii) Sezary syndrome
(iii) Primary cutaneous CD30+ T-cell lymphoproliferative disorders
(iv) Primary cutaneous anaplastic large-cell lymphoma
(v) Primary cutaneous γδ T-cell lymphoma
(vi) Primary cutaneous CD8+ aggressive epidermotropic lymphoma
(vii) Primary cutaneous CD4+ small/medium T-cell lymphoma

Nodal
(i) Angioimmunoblastic T-cell lymphoma
(ii) Anaplastic large-cell lymphoma, ALK positive
(iii) Anaplastic large-cell lymphoma, ALK negative
(iv) Peripheral T-cell lymphoma, NOS

Extranodal
(i) Systemic EBV+ T-cell childhood lymphoproliferative disorder
(ii) Hydroa vacciniforme-like lymphoma
(iii) Extranodal NK/T-cell lymphoma, nasal type
(iv) Enteropathy-associated T-cell lymphoma
(v) Hepatosplenic T-cell lymphoma
(vi) Subcutaneous panniculitis-like T-cell lymphoma

Leukemic
(i) T-cell prolymphocytic leukaemia
(ii)T-cell large-granular lymphocytic leukaemia
(iii) Adult T-cell leukaemia/lymphoma