Clinical Study
Cutaneous Polyarteritis Nodosa in Childhood: A Case Report and Review of the Literature
Table 1
Frequency of system involvement in childhood cPAN (
).
| Study | Total | Skin involvement (Subcutaneous nodules, livido reticularis, purpura, edema, and/or ulcers) | Joint involvement (Arthralgia, arthritis) | Muscle involvement (Myalgias, myositis) | Nerve involvement (Mononeuritis multiplex, peripheral neuropathy, cranial nerve palsy, and/or abnormal nerve conduction) |
| Ozen et al. [4] | | 33 (100%) | 13 (39%) | 5 (15%) | 1 (3%) | Kumar et al. [5] | | 9 (100%) | 7 (78%) | 0 (0%) | 0 (0%) | Diaz-Perez et al. [6] | | 5 (100%) | 3 (60%) | 5 (100%) | 3 (60%) | Fink [7] | | 5 (100%) | 5 (100%) | 5 (100%) | 0 (0%) | Tinaztepe et al. [8] | | 4 (100%) | 4 (100%) | 4 (100%) | 0 (0%) | Sheth et al. [9] | | 4 (100%) | 4 (100%) | 4 (100%) | 2 (50%) | Topaloglu et al. [10] | | 3 (75%) | 2 (50%) | 3 (75%) | 4 (100%) | Fathalla et al. [11] | | 4 (100%) | 3 (75%) | 0 (0%) | 0 (0%) | Kirkali et al. [12] | | 2 (67%) | 0 (0%) | 1 (33%) | 3 (100%) | Yonis [13] | | 3 (100%) | 0 (0%) | 3 (100%) | 2 (67%) | Siberry et al. [14] | | 2 (100%) | 2 (100%) | 0 (0%) | 0 (0%) | Finkel et al. [15] | | 2 (100%) | 2 (100%) | 2 (100%) | 1 (50%) | Eleftheriou et al. [3] | | 2 (100%) | 0 (0%) | 1 (50%) | 1 (50%) | Till et al. [16] | | 2 (100%) | 2 (100%) | 0 (0%) | 0 (0%) | Single case reports [17ā53] | | (95%) | (59%) | (49%) | (14%) |
| TOTAL | | 115 (96.6) | 69 (58.0) | 51 (42.9) | 22 (18.5%) |
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