Familial Syndromes Coupling with Small Renal Masses

Table 3

Clinical and pathological subtypes of familial renal carcinoma (adapted from Zbar et al. [3]).

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(1) Single clear cell renal carcinomas

(2) Bilateral multiple clear cell renal carcinomas, without VHL

(3) Single clear cell renal carcinomas and renal oncocytomas^*

(4) Single clear cell renal carcinomas and papillary renal carcinomas^**

(5) Single and multiple renal oncocytomas without the other clinical features of BHD syndrome

(6) Single or multiple bilaterally renal carcinomas but not HPRC or HLRCC

(7) Other

^*Families with some members affected with single clear cell renal carcinomas and other members affected with single renal oncocytomas

^**Families with one member affected with single clear cell renal carcinoma and another member affected with single clear cell renal carcinoma and another member affected with papillary renal carcinoma

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