Glycogen Storage Disease Type Ia in Canines: A Model for Human Metabolic and Genetic Liver Disease
Figure 2
Outline of endogenous glucose production pathways. EC = extracellular, IC = intracellular. (a) Normal pathway and function of G6Pase. (b) Alterations seen with deficiency of G6Pase (GSDIa) include lack of dephosphorylation of G6P and shunting of excess G6P to produce glycogen and lactate.
