Table 4: Plasma CS isomers levels and structure in Fabry’s patients and healthy control subjects obtained by FACE analysis of fluorophore-labeled unsaturated disaccharides.

Patients ( = 24) Controls ( = 43) Patients versus Controls ( )

CS isomers (μgUA/mL plasma)6.07 2.965.61 2.990.66
*CS charge density (%)41.9 5.942.8 8.60.72

CS charge density was evaluated as ratio between ΔDi-4S and the sum of ΔDi-nonS and ΔDi-4S.