Table 1: Clinical and neuroradiological features of CCM sporadic patients.

FeatureAll subjectsMalesFemales
40

Symptomatic subjects

Age of patients (yr)
 Mean ± SD
 Range2–7718–772–60
Age of onset (yr)
 Mean ± SD
 Range1–7118–772–60
Number of CCM lesions
 Single 311318
 Multiple5 41
Lesion seat23 supratentorial
12 subtentorial
1 supra/subtentorial
Extracerebral0
Types of first clinical manifestations
 Cerebral haemorrhages
  Cerebral haemorrhages + headache (1)4
  Cerebral haemorrhages + focal neurological deficits (3)
 Epilepsy
  Epilepsy (12) 14
  Epilepsy + focal neurological deficits (2)
 Focal neurological deficits
  Focal neurological deficits (7) 9
  Focal neurological deficits + headaches (2)
 Headaches 9

Asymptomatic subjects

Age of patients (yr)
 Mean ± SD
 Range36–64
Number of CCM lesions
 Single4
 Multiple
Lesion seat Subtentorial
Extracerebral0