Reactive Pulmonary Capillary Hemangiomatosis and Pulmonary Veno-Occlusive Disease in a Patient with Repaired Scimitar Syndrome

Figure 2

Histological pictures from the left lung (a) showing thickening of the alveolar septa due to capillary proliferation and congestion. In addition, massive iron deposition in the alveolar spaces secondary to venous obstruction is found. The Elastic van Gieson (EvG) staining (b) highlights arterialization and intimal fibrosis of venules in the interlobular septa with subtotal luminal occlusion. In contrast to the left lung, the right lung is characterized by a normal alveolar architecture with only minimal congestion (c). The EvG staining (d) shows intimal proliferation and media hyperplasia possibly related to pressure overload of the right lung but no signs of PCH or PVOD.