| Studies PCO | No | Symptoms | Site of origin (number) | Gender M/F | Age of onset Mean/range |
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Heggie et al., 2003 [33] | 2 | Pain, swelling | Unilateral mandibular enlargement (2) | 0M/8F | 10,5/7–12 | Yamazaki et al., 2007 [65] | 1 | Pain, swelling, and trismus | Corpus-ramus mandibulae (1) | 1M/0F | 9 | Lentrodt et al., 2007 [20] | 3 | Pain, swelling | Hemimandible (3) | 1M/2F | 11,5/10–13 | Bevin et al., 2008 [37] | 4 | Pain, swelling | Hemimandible (4) | 0M/4F | 25/13–52 | Theologie-Lygidakis et al., 2011 [14] | 5 | Pain, swelling, trismus, and lymphadenopathy | Angulus-ramus mandibulae (2) Corpus-angulus mandibulae (2) Maxilla and zygoma complex (1) | 1M/4F | 7/3–9 | Obel et al., 2013 [36] | 3 | Pain, swelling, and trismus | Hemimandible (3) | 1M/2F | 9/6–11 | Ventin and Eguido, 2006 [67] | 1 | Pain, erythema of skin, and paresthesia of alveolar inferior nerve | Hemimandible (1) | 1M/0F | 23 | Agarwal et al., 2014 [7] | 1 | Pain, swelling, and paresthesia of alveolar inferior nerve | Corpus mandibulae (1) | 0M/1F | 28 | Kanemoto et al., 1992 [68] | 1 | Pain, swelling, and trismus | Condyle mandibulae (1) | 1M/0F | 14 | Zemann et al., 2011 [66] | 1 | Pain, swelling, and trismus | Condyle mandibulae (1) | 0M/1F | 51 | Berglund, 2015 (The present study) | 2 | Pain, swelling, and trismus Lymphadenopathy | Corpus-condyle (1) Angulus-condyle (1) | 0M/2F | 11,5/11-12 | Total | 24 | | | 6M/18F | Mean 18.1 years |
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