Case Report
Psychological Aspects of Androgen Insensitivity Syndrome: Two Cases Illustrating Therapeutical Challenges
Table 1
Severity of androgen insensitivity.
| Grade | Syndrome | Phenotype: genitalia | Phenotype: other |
| 1 | MAIS | Male | Infertility | 2 | PAIS | Male | Mild undermasculinization, hypospadias | 3 | PAIS | Male | Severe undermasculinization, cryptorchidism, bifid scrotum | 4 | PAIS | Ambiguous | Severe undermasculinization, phallus between penis and clitoris | 5 | PAIS | Female | Separate urethral and vaginal orifices, mild clitoridomegaly | 6 | PAIS | Female | Normal pubic/axillary hair | 7 | CAIS | Female | Scarce or absent pubic/axillary hair |
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CAIS: Complete Androgen Insensitivity Syndrome, PAIS: Partial Androgen Insensitivity Syndrome, MAIS: Mild Androgen Insensitivity Syndrome.
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