Case Report

Psychological Aspects of Androgen Insensitivity Syndrome: Two Cases Illustrating Therapeutical Challenges

Table 1

Severity of androgen insensitivity.

GradeSyndromePhenotype: genitaliaPhenotype: other

1MAISMaleInfertility
2PAISMaleMild undermasculinization, hypospadias
3PAISMaleSevere undermasculinization, cryptorchidism, bifid scrotum
4PAISAmbiguousSevere undermasculinization, phallus between penis and clitoris
5PAISFemaleSeparate urethral and vaginal orifices, mild clitoridomegaly
6PAISFemaleNormal pubic/axillary hair
7CAISFemaleScarce or absent pubic/axillary hair

CAIS: Complete Androgen Insensitivity Syndrome, PAIS: Partial Androgen Insensitivity Syndrome, MAIS: Mild Androgen Insensitivity Syndrome.