Table 1: Clinical history of the twins.

ICC088 (III : 7)ICC089 (III : 6)

GenderFemaleMale
Deafness etiologyCongenitalCongenital
Suspicion of deafness18 months18 months
Diagnosis24 months24 months
Clinical historyNormal pregnancy
No associated pathologies
No previous surgical procedures
2 episodes of ear infections (otitis) prior implantation (without suppuration)
No allergies
Vaccination plan up to date
Normal pregnancy
No associated pathologies
No previous surgical procedures
No allergies
Vaccination plan up to date
AudiogramNeurosensorial bilateral profound deafness, stage 3Neurosensorial bilateral profound deafness, stage 3
Placement of hearing aids24 months24 months
Gain with hearing aidsVery poor adaptation
No language development
Good adaptation
Functional gain up to 1000 Hz
No language development
Auditory evoked potentials (AEP)Wave V present above 90 dB nHL on the right and above 100 dB nHL on the leftAbsence of AEPs until 110 dB nHL bilaterally
Computerized axial tomography scan (CAT scan)Morphologically normal and permeable cochlea
Normal inner ear canals
Morphologically normal and permeable cochlea
Normal inner ear canals
Magnetic resonance imaging (MRI)No morphological alterations
No congenital malformations
No cochlear nerve atrophy
Normal cochleas
No morphological alterations
No congenital malformations
No cochlear nerve atrophy
Normal cochleas
Age at implantation42 months42 months
Duration of CI use56 months56 months
Age at audiological tests and present study8 years8 years
CI modelCI24R CA AdvanceCI24R CA Advance
Speech processorSPRINTSPRINT
Stimulation modeMP1+2MP1+2
Stimulation strategyACEACE
Implanted earRightRight