Case Report
Primary Vulval Rhabdoid Tumor in an Adult: A Case Report, Immunohistochemical Profile and Literature Review
Table 1
Characteristics of the previously reported cases of EMRT of the vulva [
1–
10].
| Author, year | Age at diagnosis (years) | Site | Primary treatment | Reported survival (months) |
| | 19 | R LMJ | | 38 (alive) | Perrone et al., 1989§ [1] | 30 | R LMJ | Surgery | 8 (dead) | | 31 | L vulva | | 138 (dead) | Matias et al., 1990 [2] | 49 | L LMJ | Surgery + chemotherapy | 9 (dead) | Lupi et al., 1996 [3] | 39 | L LMJ | Surgery + chemotherapy + radiation | 4 (dead) | Igarashi et al., 1998 [4] | 39 | L LMJ | Surgery + chemotherapy | 8 (alive) | Sert et al., 1999 [5] | 44 | R LMJ | Surgery + chemotherapy + radiation | 8 (dead) | Brand and Covert 2001 [6] | 40 | Mons pubis | Surgery + chemotherapy + radiation | 61 (alive) | Haidopoulos et al., 2002¥ [7] | — | Clitoris | — | — | Tzilinis et al., 2002 [8] | 63 | L LMJ | Surgery + radiation | 30 (alive) | Argenta et al., 2007€ [9] | 35 | R vulva | Surgery + radiation | 40 (alive) | Narendra et al., 2010 [10] | 50 | R LMJ and mons pubis | Surgery + radiation | 30 (alive) | Current case | 25 | Mons Pubis, extending to L inguinal area | Surgery | Lost followup |
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R: right. L: left. §3 cases were reported. ¥No full text is available in PubMed. €The diagnosis given was EMRT/proximal epithelioid sarcoma.
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