Lupus-Associated Pulmonary Arterial Hypertension: Variable Course and Importance of Prompt Recognition

Table 3

Hemodynamic parameters from right heart catheterization of the patient after successful treatment of 2012 episode of PAH compared to the current presentation of severe PAH and cardiogenic shock.

Hemodynamic; parameter (units)	Reference range	Symptom-free baseline; (2012, posttreatment)	Current PAH exacerbation
RAP (mmHg)	1–6	1	7
PAWP (mmHg)	6–15	4	4
PAP (mmHg)	20–30/10–15	27/11	86/51
Mean PAP (mmHg)	10–20	17	62
CO (L/min)	4–8	7.8	4.2
CI (L/min/m^2)	2.6–4.2	4.9	2.6
PVR (Dynes-sec/cm^5)	≤240	128	784

RAP: right atrial pressure; PAWP: pulmonary artery wedge pressure; PAP: pulmonary artery pressure designated here as systolic/diastolic; CO: cardiac output; CI: cardiac index; PVR: pulmonary vascular resistance. Note: measurements made while patient was on vasopressors and inotropes for clinical and echocardiographic evidence of acute cardiogenic shock given the need for emergent hemodynamic support and stabilization before the RHC could be performed safely.