Alpha-1 Antitrypsin Deficiency Presenting with MPO-ANCA Associated Vasculitis and Aortic Dissection

Figure 1

Radiological investigations. Sagittal ((a) and (b)) and coronal ((c) and (d)) reconstructions of CT scans, demonstrating type B aortic dissection and elongated aorta before and after TEVAR. The entry tear is demonstrated at the level of thoracic 10. 18-Fludeoxyglucose PET scan (e), demonstrating large vessel vasculitis.

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(e)