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Case Reports in Otolaryngology
Volume 2012 (2012), Article ID 163851, 3 pages
http://dx.doi.org/10.1155/2012/163851
Case Report

Papillary Endolymphatic Sac Tumor: A Case Report

1Department of Pathology, All India Institute of Medical Sciences, Academic Building, Ansari Nagar, New Delhi 110 029, India
2Department of Radio Diagnosis, All India Institute of Medical Sciences, Academic Building, Ansari Nagar, New Delhi 110 029, India
3Department of Otorhinolaryngology, All India Institute of Medical Sciences, Academic Building, Ansari Nagar, New Delhi 110 029, India

Received 4 April 2012; Accepted 20 June 2012

Academic Editors: P. A. Fagan, N. Perez, and H. Yamane

Copyright © 2012 S. Arava et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

Glandular tumors involving the middle ear are rare and distinguishing between adenoma and adenocarcinoma remains difficult. A distinct subclass of these tumors demonstrates microscopic papillary architecture and has a propensity to erode the petrous bone and extend intracranially. The term “aggressive papillary middle ear tumor” has recently been proposed to describe this more invasive type of middle ear tumor. These tumors cause symptoms even when microscopic in size. Although histologically benign, they have been locally destructive with frequent intracranial extension and patients may die of uncontrolled local disease. These tumors do not metastasize but there is single case report of drop metastasis to the spine in the literature. Hence this tumor must be distinguished from other benign tumors of the middle ear. These rare neoplasms constitute a distinct pathological entity and deserve wider recognition.