Case Report

Mucoepidermoid Carcinoma Associated with Osteosarcoma in a True Malignant Mixed Tumor of the Submandibular Region

Table 1

True mixed tumor: literature review.

AuthorsYearNumber of casesSiteType of carcinomaType of sarcomaType of treatmentFollow-upRecurrence

Clapp [15]19661Parotid glandAdenocarcinomaAngiosarcomaTotal Parotidectomy

King Jr. [16]19671Submandibular glandUndifferentiated adenocarcinomaFibrosarcomaSurgical resection and radiotherapy1 yearNo local recurrence or distant metastasis

Huntington and Dardick [17]19851Parotid glandDuctal adenocarcinomaChondrosarcomaTotal parotidectomy18 monthsNo local recurrence or distant metastasis

Stephen et al. [6]1986129: parotid gland
3: submandibular gland
All ductal carcinoma10: chondrosarcoma
2: fibrosarcoma
Surgical resection in all cases

Dardick et al. [18]19891Parotid glandUndifferentiated AdenocarcinomaChondrosarcomaTotal parotidectomy

Garner et al. [19]19891Parotid glandUndifferentiated
carcinoma
Chondrosarcoma/osteosarcomaTotal parotidectomy and adjuvant radiotherapy18 monthsNo local recurrence or distant metastasis

Suzuki et al. [20]19901Submandibular glandUndifferentiated
carcinoma
Chondrosarcoma/osteosarcomaSurgical resection and radiotherapy1 yearNo local recurrence or distant metastasis

Takata et al. [21]19901TongueBasaloid carcinomaChondrosarcoma/myxosarcoma/fibrosarcomaSurgical resection and radiotherapy

Bleiweiss et al. [22]19921Submandibular glandAdenocarcinomaChondrosarcoma/osteosarcomaSurgical resection and radiotherapy1 yearLocal recurrence of the sarcomatous component

Lopez et al. [23]19941Parotid glandUndifferentiated
carcinoma
ChondrosarcomaTotal parotidectomy and adjuvant radiotherapy13 monthsNo local recurrence or distant metastasis

Carson et al. [24] 1995 2(i) Parotid glandBoth adenocarcinoma(i) Chondrosarcoma/osteosarcoma(i) Total parotidectomy + subsequent chemotherapy(i) 9 months(i) Died
from local recurrence and aspiration pneumonia
(ii) Submandibular gland(ii) Leiomyosarcoma (ii) Surgical resection(ii) 9 months (ii) No local recurrence or distant metastasis

Sironi et al. [9]20001Parotid glandSquamous cell carcinomaOsteosarcoma and myoepithelial malignant proliferationTotal parotidectomy and adjuvant radiotherapy2 yearsNo local recurrence or distant metastasis

Kwon and Gu [1]20011Parotid glandSquamous cell carcinomaRhabdomyosarcomaTotal parotidectomy and adjuvant radiotherapy12 monthsNo local recurrence or distant metastasis

Pang et al. [2]20011Parotid glandSquamous cell carcinomaChondrosarcomaTotal parotidectomy and right radical neck dissection36 monthsNo local recurrence or distant metastasis

Mardi and Sharma [4]20041Parotid glandAdenocarcinomaChondrosarcoma/osteosarcomaTotal parotidectomy16 monthsNo local recurrence or distant metastasis

Staffieri et al. [14]20071Parotid glandAdenocarcinomaChondrosarcoma/osteosarcomaSurgical resection and adjuvant chemotherapy and radiotherapy26-month follow-upNo local recurrence or distant metastasis

Morey-Mas et al. [25]19971Submandibular gland/salivary glandUndifferentiated carcinomaChondrosarcomaSurgical resection and radiotherapy15 monthsNo local recurrence or distant metastasis

Tomas et al. [3]20141Parotid glandSalivary duct adenocarcinomaMalignant fibrous histiocytomaTotal parotidectomy and radiotherapy9 monthsNo local recurrence or distant metastasis

Taki et al. [5]20131Parotid glandSquamous cell carcinomaChondrosarcomaSurgical resection and adjuvant radiotherapy14 monthsNo local recurrence or distant metastasis