Case Reports in Pathology / 2013 / Article / Tab 1 / Case Report
Cutaneous Epithelioid Clear Cells Angiosarcoma in a Young Woman with Congenital Lymphedema Table 1 Clinical features of patients with cutaneous angiosarcoma associated with congenital lymphedema described in the literature (modified from Offori et al., 1993 [
12 ] and Bernardi et al., 2009 [
18 ] ).
Author Sex Age at diagnosis Tumor site Clinical appearance Interval in diagnosis Treatment Survival Kettle [19 ] F 44 y RL Blue-red dislocation Not stated Amputation Not stated Liszauer et al. [20 ] M 28 y RLL Ulcerated lesion 4 m Local excision Died at 11 m Scott et al. [21 ] F 50 y LUL Papillomatous nodules >7 m Local excision/amputation Died at 37 m Taswell et al. [22 ] M 17 y LUL Ulcerated lesion Not stated Disarticulation Died at 24 m Bunch [23 ] F 13 y UL Not stated Not stated Interscapular amputation Died at 1 y Finlay-Jones [24 ] M 34 y LLL Ulcerated blue tumor Not stated Excision and combined therapy Died at 31 m Merrick et al. [25 ] M 52 y LUL Swelling/blue nodules 6 m Wide local excision/amputation/radiotherapy Died at 36 m Mackenzie [26 ] M 64 y RLL Nodules/ulceration 2 m Hindquarter amputation/radiotherapy Alive at 24 m Dubin et al. [27 ] F 29 y LUL Ulcerated lesion 3 y Disarticulation Died at 45 m Laskas et al. [28 ] F 85 y RUL Purple papules and blisters/ulceration 10 m Palliative midhumeral amputation Died at 14 m Banathy et al. [29 ] F 50 y LUL Purple nodules Not stated Midhumeral amputation Died at 26 m Sordillo et al. [30 ] F 23 y Not stated Not stated Hemipelvectomy Alive at 19 y Bostrom et al. [31 ] F 19 y RUL Infected lesion 4 m Amputation/disarticulation Died at 12 m F 10 y LLL Blue/red nodules 8 m Amputation/disarticulation Alive at 10 m Offori et al., 1993 [12 ] F 43 y LLL Blue/purple nodules 2 m Amputation Alive at 9 m Andersson et al. [32 ] M 35 y RL Blue nodules Not stated Hemipelvectomy, chemotherapy Not stated Cerri et al. [33 ] F 42 y Pubis Ecchymotic plaque Not stated Hemipelvectomy, radiotherapy Not stated Bernardi et al. [18 ] F 4 y LLL Ulcerated lesion/blue nodules 1 y Local excision Alive at 14 m Deyrup et al., 2011 [14 ] F 2 y Foot Not stated Not stated Local excision Died at 1 y Present case F 21 y Groin Purple/reddish infiltrated and ulcerated mass 10 m Local excision Died at 3 m
LLL: left lower limb; RLL: right lower limb; LUL: left upper limb; RUL: right upper limb; m: months; and y: years.