Tracheal Resection for Critical Airway Obstruction in Morquio A Syndrome

Figure 1

CT angiogram sagittal and (b) axial views immediately above and (c) below the manubrial head demonstrate multifactorial airway obstruction. Abnormal manubrium orientation and interposed brachiocephalic vasculature compressing the midtrachea into the c-spine, tracheal tortuosity, and tracheal ring deformity; shortened thorax with upper mediastinal compression; and cervico-thoracic kyphoscoliosis. (d-e) 3D-reconstructed images clearly demonstrate a tight thoracic inlet narrowing ().