Tracheal Resection for Critical Airway Obstruction in Morquio A Syndrome

Figure 2

Clinical photographs at cricotracheal resection: (a) tracheal exposure via limited manubriectomy showed a first bend 36 mm distal to the glottis, leading into a 16 mm tortuosity terminating 28 mm above the carina. (b) The deformed tracheal segment, which had concertinaed leading to omega-shaped tracheal ring buckling, was resected without (c) cardiopulmonary bypass,

(a)

(b)

(c)