Multisystem Radiologic Manifestations of Erdheim-Chester Disease

Figure 10

A 35-year-old male with axial and coronal reformatted contrast-enhanced CT images of the abdomen and pelvis showing enhancing soft tissue infiltration of the adrenal glands and kidneys (hairy kidney appearance) bilaterally (thin arrows). This is causing constriction of the renal pelvis and proximal ureters resulting in hydronephrosis. There is also retroperitoneal soft tissue infiltration (thick arrow) covering the posterolateral aorta (coated aorta appearance) which extends from just below level of renal arteries to aortic bifurcation and proximal right common iliac artery.