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Author | Age (yrs) (at event) | Gender | Clinical history and prebleeding therapies | Antibody profile | Site of bleeding(s) | Treatment | Outcome (as reported) |
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Orrell et al. [7] | 50 | Female | DM age 34 Corticosteroid Azathioprine IVIG | None specified | Left rectus abdominis | Blood transfusions Prednisone Azathioprine | Survived, no recurrent bleeding |
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Orrell et al. [7] | 11 | Female | DM age 8 Prednisone | ANA 1 : 320 speckled | Retroperitoneum, posterior to right ascending colon | Supportive | Survived without recurrence |
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Fang et al. [8] | 65 | Female | PM age 65 Hydrocortisone Prednisone | ANA 1 : 320 speckled | Retroperitoneum, superior duodenal pancreatic artery, SMA | Angiography with embolization | Expired from sepsis without rebleeding |
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Yamagishi et al. [9] | 64 | Female | DM/ILD age 64 Solumedrol Prednisone Cyclosporine Dalteparin | ANA positive Elevated serum KL-6 | Retroperitoneum, right psoas, right iliacus, left rectus sheath | Angiography with embolization with rebleeding and repeat embolization | Expired from TTP and multiorgan failure |
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Higashi et al. [10] | 77 | Female | DM age 77 Solumedrol Prednisone Cyclosporine Heparin | Elevated serum KL-6 | Retroperitoneum, left iliopsoas, left iliacus, right sternomastoid | Supportive | Expired from DIC |
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Van Gelder et al. | 50 | Male | DM/ILD age 50 Solumedrol IVIG | Anti-Ro52 | Retroperitoneum, right iliacus, right psoas | Transfusions Solumedrol | Expired from multiorgan failure |
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Van Gelder et al. | 63 | Female | DM/ILD age 63 Solumedrol IVIG | Anti-SSA Anti-Ro52 | Retroperitoneum, right pectineus, right iliopsoas | Transfusions Solumedrol Cytoxan | Expired from multiorgan failure |
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