Case Report

An Unusual Case of Systemic Lupus Erythematosus and Hemophagocytic Syndrome

Table 2

Additional labs.

VariableMeasurementReference range

DAT broad spectrum Coombs Ser (Direct Coombs)NegativeNegative
GGT10012–58 U/L
Tryptase42–10 ng/mL
Lipase2223–300 U/L
Uric acid7.13.5–8.5 mg/dL
Lactic acid7.40.7–2.1 mmol/L
Ammonia429–30 μmol/L
CryoglobulinNegativeNegative
Creatine kinase92055–170 U/L
CRP, high sensitivity10.4Null
Sedimentation rate1000–13 mm/hr
LDH2387313–618 U/L
ADAMTS13 Activity8468–163% activity
G6PDAdequateAdequate
Haptoglobin, quant2230–200 mg/dL
Ferritin700.722.0–322.0 ng/mL
Iron4149–181 μg/dL
Iron binding capacity, total (TIBC)265261–462 μg/dL
Thyroid stim. hormone10.55–4.78 mIU/mL
Cortisol AM16.544.0–22.0 μg/dL
Factor XI assay6650–150%
Factor X assay6650–150%
Factor II activity6470–150%
Factor VIII assay27950–150%
Factor VII assay1650–150%
Factor V assay4950–150%
Fibrinogen123225–483 mg/dL
D-dimer13.29<0.5 μg/mL