Case Report
Postcardiotomy Mechanical Circulatory Support in Two Infants with Williams’ Syndrome
| | Case 1 | Case 2 |
| Age (months) | 8.5 | 13 | Gender | Male | Female | Weight | 6.7 kg | 9 kg | Height | 71 cm | 70 cm | Primary diagnosis | Supravalvular aortic stenosis, Williams’ syndrome | Supravalvular aortic stenosis, pulmonary artery stenosis, Williams-Beuren syndrome | CPB time | 226 min | 159 min | Ischaemic time | 61 min | 54 min | ECMO support | 70 hrs | 44 hrs | APPT (for ACT 140–180) | 48.9* (32.3–>110) | 35.2* (31.4–89.4) | Complications | Haemorrhage and reexploration | Pneumothorax | ICU stay | 9 days | 30 days | Total stay | 16 days | 39 days |
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Median value.
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