| No. | Age | Diagnosis | ACR Criteria+ | Previous drugs | PR3 (U/mL) | MPO (U/mL) | Creatinine (mg/dL) | CRP (mg/dL) | Maintenance therapy | BVAS | VDI | Gender | Disease duration | Renal histology | ANCA |
| 1 | 75 | GPA | Renal, lungs | Cyc | 24 | neg | 3.54 | 18.1 | Cyc, Prednisone | 12 | 10 | m | 2 month | Renal involvement but no renal biopsy performed | 1 : 80 | 2 | 66 | GPA | ENT, lungs | Cyc, MTX | 11 | neg | 0.93 | 10.5 | Cyc, Prednisone | 7 | 5 | m | 10 years | No biopsy | 1 : 20 | 3 | 61 | GPA | ENT, lungs, renal | Cyc, MTX | neg | neg | 0.99 | 3.1 | Prednisone | 10 | 6 | m | 15 years | Focal segmental necrotizing glomerulonephritis | 1 : 20 | 4 | 75 | GPA | Lungs, renal | none | 301 | neg | 3.31 | 112 | Prednisone, PS | 19 | 3 | m | 1 day | Focal segmental necrotizing glomerulonephritis | 1 : 640 | 5 | 51 | GPA | ENT, lungs | Cyc, MMF | neg | neg | 0.9 | 3 | Prednisone | 5 | 5 | f | 4 years | Renal involvement but no renal biopsy performed | 1 : 20 | 6 | 67 | GPA | ENT, lungs, renal | Cyc, MTX | 9 | neg | 1.2 | 5.7 | Lefl, Prednisone | 9 | 9 | m | 22 years | Renal involvement but no renal biopsy performed | 1 : 40 | 7 | 56 | GPA | ENT, lungs | Prednisone, AZA | 25 | neg | 0.8 | 2 | Prednisone, AZA | 8 | 3 | f | 2 month | No biopsy | 1 : 160 | 8 | 58 | GPA | ENT, lungs | MTX | neg | neg | 0.57 | 2 | Prednisone, AZA | 5 | 12 | f | 8 years | No biopsy | neg | 9 | 62 | GPA | ENT, lungs, renal | Cyc | neg | neg | 1.02 | 2 | Prednisone, AZA | 4 | 5 | m | 8 years | Focal segmental necrotizing glomerulonephritis | neg | 10 | 42 | GPA | ENT, ENT granulomas | Cyc, MTX | 11 | neg | 0.84 | 3.5 | Cyc, prednisone | 7 | 7 | f | 2 years | No biopsy | 1 : 20 | 11 | 32 | GPA | ENT, ENT granulomas | Cyc, AZA, Infli | 5.3 | neg | 0.83 | 18.4 | Prednisone, MMF | 7 | 8 | f | 5 years | No biopsy | 1 : 20 | 12 | 57 | GPA | Lungs, renal | Cyc, MTX | neg | neg | 1.72 | 3.3 | Prednisone, MMF | 10 | 7 | m | 12 years | Focal segmental necrotizing glomerulonephritis | 1 : 20 | 13 | 30 | GPA | Lungs, renal | Cyc, AZA, PP | 6.4 | neg | 0.9 | 2.2 | AZA | 6 | 1 | m | 4 years | Focal segmental necrotizing extracapillary proliferating glomerulonephritis with intermediate interstitial nephritis | 1 : 20 | 14 | 70 | GPA | Lungs, renal | Cyc, AZA | neg | neg | 4.14 | 2 | Prednisone, AZA | 10 | 8 | f | 8 years | Focal segmental necrotizing, extracapillary proliferating glomerulonephritis | neg | 15 | 72 | GPA | ENT, lungs | Cyc | 88 | neg | 2.35 | 4.7 | Prednisone, AZA | 21 | 6 | m | 10 years | Renal involvement but no renal biopsy performed | 1 : 320 | 16 | 25 | GPA | ENT, renal | Cyc, PS | 25 | neg | 1.14 | 4.5 | Cyc, Prednisone | 13 | 3 | m | 5 years | Focal segmental necrotizing, intra- and extracapillary proliferating glomerulonephritis | 1 : 80 | 17 | 69 | GPA | ENT, lungs | Cyc, AZA, MTX | 6.8 | neg | 1.17 | 2 | Prednisone | 2 | 7 | m | 9 years | No biopsy | 1 : 20 | 18 | 56 | GPA | ENT, lungs, renal | Cyc, AZA | neg | neg | 0.67 | 2 | AZA | 7 | 3 | m | 6 years | Focal segmental necrotizing glomerulonephritis | 1 : 80 | 19 | 53 | GPA | Lungs, renal | Cyc,AZA | 5 | neg | 2.11 | 2.1 | Prednisone, AZA | 4 | 6 | m | 7 years | Focal segmental necrotizing extracapillary proliferating glomerulonephritis with mild interstitial nephritis | neg | 20 | 84 | GPA | ENT, lungs, renal | Cyc, Prednisone | 12 | neg | 1.64 | 68 | Prednisone | 7 | 5 | m | 10 years | Renal involvement but no renal biopsy performed | 1 : 40 | 21 | 83 | GPA | Lungs, renal | MMF, Prednisone | 7 | neg | 1.05 | 7 | MMF, Prednisone | 2 | 8 | m | 2 years | Renal involvement but no renal biopsy performed | 1 : 20 | 22 | 80 | GPA | Renal, renal histology | Cyc, Prednisone | 5.5 | neg | 2.0 | 9.9 | None | 3 | 2 | f | 10 years | Focal segmental necrotizing. extracapillary proliferating glomerulonephritis | 1 : 80 | 23 | 69 | GPA | ENT, lungs, renal | Cyc, AZA | 260 | neg | 1.08 | 6.4 | AZA | 4 | 4 | f | 6 years | Focal segmental glomerulosclerosis with chronic interstitial nephritis | 1 : 320 | 24 | 65 | GPA | ENT, lungs | Cyc, Prednisone | 1.1 | neg | 0.83 | 7.1 | Prednisone, MTX | 3 | 5 | f | 5 years | No biopsy | neg | 25 | 64 | GPA | Lungs, renal | Cyc, PP, AZA | 16 | neg | 1.94 | 5 | Prednisone, MMF | 9 | 9 | f | 4 month | Focal segmental necrotizing glomerulonephritis | 1 : 40 | 26 | 71 | MPA | Lungs, polyneuropathy, arthralgia | Cyc | neg | 87 | 1.04 | 15.5 | Prednisone | 15 | 5 | m | 6 month | No biopsy | 1 : 80 | 27 | 86 | MPA | Lungs, renal, polyneuropathy | Cyc, PP | neg | 134 | 0,79 | 40 | Cyc | 7 | 2 | m | 7 years | Focal segmental necrotizing glomerulonephritis | 1 : 40 | 28 | 76 | MPA | Renal | Cyc | neg | 88 | 1.58 | 2 | Prednisone | 4 | 5 | f | 11 years | No biopsy | 1 : 80 | 29 | | MPA | Lungs, poyneuropathy | Cyc, PS | neg | 67 | 0.88 | 9.6 | Prednisone, Cyc | 15 | 3 | m | 3 month | No biopsy | 1 : 40 | 30 | 76 | MPA | Renal | MMF | neg | 75 | 1.93 | 4.3 | Prednisone, MMF | 7 | 2 | m | 2 years | No biopsy | 1 : 20 | 31 | 57 | MPA | Arthralgia | Prednisone | neg | 71 | 0.84 | 2 | Prednisone | 1 | 0 | f | 1 year | No biopsy | 1 : 20 | 32 | 61 | MPA | ESRD, lungs | AZA, MMF | neg | 44 | 6.75 | 11.4 | Prednisone | 9 | 6 | f | 6 years | No biopsy | 1 : 160 | 33 | 73 | MPA | Lungs, renal, neurologic | Cyc, PP | neg | 195 | 0.87 | 32.5 | Prednisone, Cyc | 13 | 10 | f | 1 year | No biopsy | 1 : 320 | 34 | 72 | MPA | Arthralgia | Prednisone | neg | 110 | 1.02 | 2 | none | 2 | 2 | f | 4 years | No biopsy | 1 : 160 | 35 | 86 | MPA | Arthralgia | Cyc | neg | 200 | 5.1 | 37.2 | Prednisone, Cyc | 14 | 4 | f | 8 years | No biopsy | 1 : 160 |
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