Exercise Stress Testing in Children with Metabolic or Neuromuscular Disorders

Table 3

Biochemical measurements of patients during the PXT test.

Subject	Time (min)	Glucose (mmol/L)	Lactate (mmol/L)	FFA (mmol/L)	3-Keto-B (mmol/L)	3-OH-B (mmol/L)	CK (U/L)	Ammonia (𝜇mol/L)
1	0	4.9	4.3^∗	0.51	0.14	0.0	116
	30	4.4	4.6^∗	0.52	0.13	0.02	115
	60	5.7^∗	2.8^∗	0.489	0.12	0.02	119
	75	5.6	3.1^∗	0.536	0.12	0.02	119
	90	6.7^∗	2.9^∗	0.559	0.12	0.02	121
	15 after	7.4^∗	4.1^∗	0.792	0.13	0.04	121
	30 after	7.5^∗	4.9^∗	0.666	0.12	0.04	118
3	0	5.5	1.8	0.08	0.0	0.0	166	22
	30	5.9	1.2	0.14	0.0	0.0	181^∗
	60	5.8^∗	0.8	0.23	0.0	0.0	186^∗
	75	6.9^∗	1.2	0.36	0.09	0.04	187	275^∗
	15 after	6.9	2.3	0.25	0.0	0.03	183^∗
	30 after		2.0	0.26	0.0	0.0	184^∗	144^∗
6	0	4.6	3.2*	0.268	0.12	0.0	48
	30	4.6	1.3	0.302	0.1	0.0	46
	60	4.4	1.4	0.444	0.12	0.0	48
	15 after	4.6	1.1	0.503	0.13	0.03
	30 after	4.7	0.9	0.528	0.13	0.03	51
7	0	7.1	1.1	0.76	0.07	0.09	103
	30	5.6	1.2	0.28	0.0	0.0
	60	4.9	1.0	0.49	0.0	0.0	98
	75	4.8	1.3	0.88	0.05	0.05	105
	90	5.5	1.1	1.03	0.10	0.12	119
	30 after	4.8	1.0	0.93	0.15	0.26	117
8	0	5.2	2.0	0.15	0.0	0.0	58
	30	4.6	0.9	0.31	0.0	0.0
	60	4.3	0.9	0.62	0.07	0.04	80
	75	4.4	1.0	0.91			78
	30 after	4.5	1.2	1.34	0.14	0.24	78
9	0	6.4	1.4	0.22	0.09	0.03	90	14
	30	4.9	1.4	0.18	0.0	0.0	93
	60	4.7	1.3	0.21	0.0	0.0	89
	75	4.4	1.1	0.42	0.0	0.0	99	22
	90	4.9	1.1	0.64	0.11	0.11	91
	15 after	4.8	0.8	0.69	0.13	0.18	92
	30 after	4.6	1.0	0.55	0.14	0.2	92	14
10	0	4.0	2.4^∗	0.20	0.11	0.10^∗	138	20
	30	3.7^∗	8.6^∗	0.21	0.11	0.11^∗	156
	60	3.5^∗	9.6^∗	0.31	0.14	0.13	151
	75	3.6^∗	9.5^∗	0.49	0.16	0.16	156	20
	90	3.6^∗	9.7^∗	0.71	0.16	0.18	157
	15 after	4.1	7.0^∗	0.72	0.113	0.29	145
	30 after	4.0	4.7^∗	0.73	0.18	0.29	146
11	0	5.9	1.4	0.41	0.0	0.0	5020^∗	7.0
	30	4.8	1.4	0.19	0.0	0.0	4975^∗
	15 after	5.3	1.4	0.57	0.0	0.0	5036^∗
	30 after	5.2	1.3	0.5	0.0	0.0		18
12	0	5.1	1.1	0.15	0.0	0.0	695^∗	33^∗
	30	5.3	1.2	0.08	0.0	0.0	776^∗
	60	5	1.2	0.11	0.0	0.0	774^∗
	75	5.1	1.4	0.16^∗	0.0	0.0	771^∗	51^∗
	90	5.0	1.7	0.23	0.0	0.0	766*
	15 after	5.1	1.1	0.76	0.0	0.0	755*

Legend: FFA: free fatty acids, 3-keto-B: 3-ketobutaric acid, 3-OH-B: 3-hydroxybutaric acid, ∗: significantly different from normal.