|
| Case | Vasculitis | Age/Sex | Ag at
SSc Dx | SSc type | Age at Vasculitis Dx | Presentation | Diagnosis | Outcome |
|
| Pathak and Gobor [29] | CNS | 45/F | 21 | L | 45 | Headache, confusion, seizure, aphasia; right face/arm/leg numbness | Angiography with abrupt cutoff in MCA branch, narrowing in ACA and MCA branches; leptomeningeal biopsy negative | Improved with methylprednisolone then cyclophosphamide |
|
| Kang et al. [28] | PAN | 28/F | 28 | D | 28 | Brownish tender nodules on legs | Skin biopsy: necrotizing arteritis in deep dermis | Stable on weekly methotrexate 20 mg |
|
Jiménez López
et al. [30] | Mixed CG | 50/F | 50 | L | 50 | Paresthesias, vision changes, aphasia, delirium; rash on lips, palms, soles | Cryoglobulin /100mL Electroencephalogram: generalized slowing Cerebral angiogram: normal | ? |
|
| Barrett et al. [31] | CF | 49/M | 38 | L | 49 | Sudden onset gangrene of fingers and toes; confusion | Cryofibrinogen 435 mg/L 40 | Died despite Subcutaneous heparin and prostaglandin E1 |
|
| Choy et al. [32] | BD | 54/F | 54 | D | 16 | Oral/genital ulcers, superficial thrombophlebitis, rash, esophageal dysmotility, no tear production, left knee arthritis | Grade II esophagitis ILD with restrictive PFTs Rash with pathergy | Unresponsive to topical steroids; later azathioprine 100 mg daily, eye drops, D-penicillamine, colchicine; arthritis continued |
|
| Yokota et al. [33] | BD | 62/M | 57 | L | 60 | Oral/genital ulcers, erythema nodosa, esophageal and gastric ulcers, chronic hepatitis C, pancytopenia | ? | Esophageal ulcers resistant to prednisolone 30 mg daily;
died from pneumonia |
|
| Sugisaki et al. [34] | RPC | 35/M | 31 | L | 35 | Left auricular ulcer and swelling; polyarthralgia | MRI: partial defect in
nasal septum | Improved with prednisolone 15 mg daily and not with antibiotics |
|
