Vasculitis in Systemic Sclerosis

Table 3

Eleven new cases of ANCA-associated vasculitis in SSc.

Case	Age/Sex	SSc (yrs)	SSc to; AAV (yrs)	SSc type	Use of; D-penicillamine	Renal	Pulm fibrosis	ANA	Scl-70	MPO
Marlier et al. [48]	62/M	5	5	L	Yes	CGN	No	?	?	+
Martínez Ara et al. [49]	63/F	2	2	?	No	CGN	No	1 : 640	+	+
Herrera-Esparza et al. [50]	60/M	2	3	L	No	CGN	No	1 : 2560	?	+
Hidalgo-Tenorio et al. [51]	48/F	1	1.5	D	No	None	Yes	1 : 320	Neg	+
	71/F	?	?	L	No	None	No	1 : 320	Neg	+
Kamen et al. [52]	45/M	0.42	0.42	D	No	CGN	No	1 : 2560	+	+
	19/M	5	5	D	Yes	CGN	No	1 : 2560	+	+
	60/F	8	8	D	No	CGN	No	?	+	+
Arnaud et al. [53]	46/F	10	5.75	D	Yes	CGN	Yes	>1 : 1000	+	+
Ramaswami et al. [54]	52/F	?	0.83	D	No	CGN	No	1 : 640	?	?
Veetil and Schimmer [55]	62/F	7	7	D	Yes	CGN	No	?	?	+

Note: All but Ramaswami had positive MPO, and none had PR3. SSc = Systemic sclerosis; L = Limited; D = Diffuse; CGN = crescentic glomerulonephritis; ? = unknown.