Clinical Study
IgG4-Related Disease Is Not Associated with Antibody to the Phospholipase A2 Receptor
Table 1
IgG4-RD patients’ characteristics.
| Patient | Age | Sex | Serum IgG4 mg/dL | Serum IgG mg/dL | ANA | Prednisonetreatment | Organ involved |
| 1 | 67 | M | 1340 | 2450 | +1 : 1280 S | Yes | aorta, lymph node | 2 | 76 | M | 2050 | 2310 | +1 : 40 S | Yes | pancreas, biliary tract, aorta, lymph node, salivary gland | 3 | 55 | M | 1500 | 1640 | +1 : 160 S | Yes | lacrimal and salivary glands | 4 | 51 | F | 401 | 726 | +1 : 5120 C | Yes | lacrimal and salivary glands | 5 | 60 | M | 365 | 2570 | +1 : 40 S | Yes | aorta | 6 | 58 | M | 894 | 1210 | +1 : 40 S | No | lymph node | 7 | 41 | M | 200 | 766 | +1 : 40 H | No | lymph node | 8 | 24 | M | 47 | 100 | — | Yes | orbital tissue | 9 | 72 | F | 429 | 1170 | +1 : 320 S | Yes | lacrimal & salivary glands Skin | 10 | 52 | F | 62 | 1280 | — | Yes | biliary tract | 11 | 40 | F | 98 | 1090 | +1 : 160 S | Yes | pancreas, lung, thyroid, lacrimal gland | 12 | 59 | M | 27 | 1280 | +1 : 40 S | Yes | retroperitoneum | 13 | 48 | F | 9 | 1240 | +1 : 40 S | No | pericardium | 14 | 63 | M | 386 | 1500 | +1 : 40 S | Yes | retroperitoneum, kidney | 15 | 56 | M | 670 | 1980 | +1 : 640 H | Yes | orbital tissue | 16 | 74 | F | 28 | 1830 | +1 : 40 S | Yes | kidney, lacrimal gland, pancreas, and biliary tract | 17 | 39 | M | 53 | 1460 | +1 : 40 S | Yes | retroperitoneum | 18 | 51 | F | 68 | 1190 | +1 : 40 S | No | lymph node | 19 | 33 | F | 139 | 1570 | +1 : 160 S | No | lymph node | 20 | 58 | F | 194 | 1160 | +1 : 40 H | Yes | tonsils | 21 | 41 | F | 240 | 1710 | +1 : 160 H | No | salivary gland | 22 | 63 | F | 30 | 923 | +1 : 320 S | Yes | orbital tissue | 23 | 51 | F | 80 | 1300 | — | Yes | pachymeninges | 24 | 82 | M | 59 | 1180 | — | No | lymph node | 25 | 66 | F | 154 | 769 | +1:160 S | Yes | retroperitoneum, lymph node, salivary gland | 26 | 72 | M | 12 | 1000 | +1 : 40 S | Yes | pancreas, salivary gland | 27 | 70 | M | 164 | 1230 | +1 : 160 S | Yes | pancreas, biliary tract, salivary gland | 28 | 61 | M | 50 | 1650 | +1 : 160 S | Yes | pancreas, retroperitoneum, hard palate, lymph node |
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S: Speckled H: Homogeneous C: Centromere.
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