Clinical Study

Development of an IgG4-RD Responder Index

Table 1

Diseases commonly associated with IgG4-related disease.

IgG4-related spectrum diseases

Idiopathic hypertrophic pachymeningitis
Orbital pseudotumor
Mikulicz’s disease
Kuttner’s tumor
Eosinophilic angiocentric fibrosis
Riedel’s thyroiditis
Idiopathic cervical fibrosis
Pulmonary inflammatory pseudotumor
Chronic sclerosing aortitis
Inflammatory abdominal aortitis
Autoimmune pancreatitis
Sclerosing cholangitis
Retroperitoneal fibrosis
Inflammatory pseudotumor of the kidney