Clinical Study

IgG4-Related Perineural Disease

Table 1

Clinical characteristics, laboratory data, and initial dose of steroid.

CaseAgeGenderSymptomIgG (mg/dL)*IgG4 (mg/dL)ANA (titer)IgE (IU/mL)Initial dose of steroid

155MaleDouble vision, subcutaneous nodule in cheek48452050×4098830 mg/day
253MaleLeft proptosis, double visionNA372×40NA30 mg/day
361MaleLacrimal gland enlargement1450463<40460820 mg/day
444MaleRight proptosis, double vision, lacrimal gland enlargement1146325<4015130 mg/day
558MaleEpigastralgia28501280NANA30 mg/day
674MaleLacrimal gland enlargement, cervical lymph node enlargement60242550NANA30 mg/day
761MalePalpable left cervical mass, lacrimal gland enlargement,73643440×2560114640 mg/day

NA: not analyzed; *normal range < 1600 mg/dL; normal range < 135 mg/dL; normal range < 170 IU/mL.