Capability and Limitations of Recent Diagnostic Criteria for Autoimmune Pancreatitis

Table 4

Japanese clinical diagnostic criteria for AIP 2011 [14].

(1) Pancreatic enlargement
a: Diffuse type
b: Segmental/focal type
(2) Narrowing of the main pancreatic duct on ERP
(3) Serum IgG4 ≥ 135 mg/dL
(4) Histology (LPSP)
a: ≥3 criteria
b: 2 criteria
(5) Other organ involvement
Sclerosing cholangitis, sclerosing  dacryoadenitis/sialoadenitis, or retroperitoneal fibrosis
(6) Effectiveness of steroid therapy
Definite diagnosis
4a histology
Diffuse type
1a + <3/4b/5>
Segmental/focal type
1b + 2 + two or more of <3/4b/5>
1b + 2 + <3/4b/5> + 6
Probable diagnosis
Segmental/focal type
1b + 2 + <3/4b/5>
Possible diagnosis
1 + 2 + 6