Research Article

Are There Clinical Differences in Limited Systemic Sclerosis according to Extension of Skin Involvement?

Table 2

Clinical and serological profiles comparing acrosclerosis and diffuse subsets.

Subset of SScAcrosclerosis ( = 29)Diffuse ( = 56)  (acro. versus diffuse)

Females, (%)25 (86,2)49 (87,5)1
Age at diagnosis, years, mean (SD)54,9 (16,2)53 (18,3)0,7
Duration of Raynaud’s prior to diagnosis, years, mean (SD)5,5 (1)1,9 (0,8)0,2
Anti-Scl-70, (%)11 (39,3)18 (43,9)0,8
Anticentromere, (%)5 (17,9)2 (4,8)0,1
Nucleolar ANA, (%)1 (3,6)9 (20,9)0,07
Upper GI involvement, % 81,364,30,5
Interstitial lung disease, %5065,30,2
Pulmonary hypertension + interstitial lung disease, %015,40,3
Isolated pulmonary hypertension, %4,82,60,3
Cardiac ultrasound abnormalities (aside from PHT), %4,5100,6
Digital ulcers, %34,532,11
Renal crisis, 011