Ehlers-Danlos Syndrome, Hypermobility Type: An Underdiagnosed Hereditary Connective Tissue Disorder with Mucocutaneous, Articular, and Systemic Manifestations

Figure 3

Orthopedic features of Ehlers-Danlos syndrome, hypermobility type. Active joint hypermobility at the fingers (a), toes (b), elbow (c), and knees (genu recurvatum, (d)). Passive hyperextension at great toe (e) and heel (f). Structural changes due to joint instability: fixed subluxation of the distal ulna (g), asymptomatic fixed subluxation of the elbow (h), fixed subluxation of the first metacarpal (i), hindfoot pronation and midfoot eversion in an 11-year-old boy (j), and hallux valgus in a 24-year-old woman (k).

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