Table 5: Additional neuropathological states and conditions in which FNS is invariably part of the neurological syndrome [2224].

Subcortical gray matter
 HIV dementia
 Wilson’s disease
 Huntington’s
 Neuroacanthocytosis syndrome
 Prionopathies (Creutzfeldt-Jakob, GSS FFI, and BSE)
 Fahr’s syndrome—calcification of the BG
 Pantothenate kinase 2 associated neurodegeneration (PANK2)
 Adult neuronal ceroid lipofuscinosis
Subcortical white matter
 Leukodystrophy disorders (metachromatic, Krabbe’s, adrenal, orthochromatic)
 Fabry’s disease
 Vanishing white matter disease
Mixed cortical and subcortical pathology
 Vasculitides
 Meningitis/encephalitis
 CADASIL
 Alexander’s disease
 Canavan disease
 Cerebrotendinous xanthomatosis
 Polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy (PLOSL) or Nasu-Hakola disease
 Mitochondrial diseases (MELAS, MERFF, and Kearns Sayre)