International Scholarly Research Notices / 2014 / Article / Tab 1 / Review Article
Pediatric Sclerosing Rhabdomyosarcomas: A Review Table 1 Showing clinicopathological features of 21 cases of pediatric sclerosing rhabdomyosarcomas reported in the literature (including present case).
Case number Author Year Age/ sex Site Size (cm) Mets (1) Primary Rx Adj. Rx Local recurrence Mets (2) TTR/TTM (mos) Rx of Rec/Mets F/U (mos) Outcome 1 Folpe et al. [8 ] 2002 18/M Orbit NA (−) Excision (−) (−) Intra-abdominal and lymph nodes 48 CT 60 Died 2 Vadgama et al. [9 ] 2004 3/F Ischiorectal fossa/buttock 3.2 (−) Excision CT (−) (−) (−) (−) 4 AWD 3 Chiles et al. [7 ]
2004 6/M Arm NA NA NA NA (+) (−) 20 NA 39 Alive with disease 4 11/M Elbow NA (−) NA NA (−) (+) 20 NA 37 Dead 5 7/F Pharynx NA (−) NA NA (+) (−) 4 NA 16 Alive with disease 6 10/F Orbit NA (−) NA NA (−) (−) (−) (−) 18 AWD 7 3/M Leg NA (−) NA NA (−) (−) (−) (−) 10 AWD 8 8/F Sinus NA (−) NA NA (−) (−) (−) (−) <1 AWD 9 16/F Thigh NA (−) NA NA (−) (−) (−) (−) 25 AWD 10 4/F Scapula NA (−) NA NA (−) (−) (−) (−) NA NA 11 12/M Masseter NA (−) NA NA (−) (−) (−) (−) <1 AWD 12 9/M Orbit NA (−) NA NA (−) (−) (−) (−) 43 AWD 13 4/M Neck NA (−) NA NA (−) (−) (−) (−) 37 AWD 14 0.3/M Retroperitoneum NA (−) NA NA (−) (−) (−) (−) NA NA 15 5/M Scrotum NA (−) NA NA (−) (−) (−) (−) 24 AWD 16
Zambrano et al. [11 ]
2006 8/F Intra-abdominal 10.5 (−) CT f/b Excision (−) NA NA NA NA NA NA 17 18/M Thigh NA NA NA NA NA NA NA NA NA NA 18 17/M Lower leg 9.0 NA CT f/b Excision NA NA NA NA NA NA NA 19 Wang et al. [10 ]
2008 12/F Nasal cavity 4.0 (−) Excision (−) (+) (−) 3 Excision + CT 5 AWD 20 Bouron-Dal Soglio et al. [6 ] 2009 7/M Deltoid 3.7 (−) Excision CT (+) Lung, Lymph nodes 24 Excision + SCT 72 Alive with Disease 21 Present case 2013 11/M Skull base 9.3 (−) Excision CT + RT (+) Spinal leptomeningeal 14 RT + CT 16 Alive with Disease
AWD: alive without disease; CT: chemotherapy; RT: radiotherapy; NA: not available; Mets (1): metastases at presentation; Mets (2): metastases during follow-up; Adj.: adjuvant; Rx: treatment; f/b: followed by; SCT: stem cell transplantation; mos: months; Rec: recurrence; TTR: time to recurrence; TTM: time to metastases.