Review Article

Cholangiocarcinoma: Biology, Clinical Management, and Pharmacological Perspectives

Table 1

Classification of cholangiocarcinomas (CCA).

Anatomical locationMacroscopic growth pattern

Intrahepatic (iCCA)Mass-forming
Periductal-infiltrating
Intraductal
Mixed (mass-forming + periductal-infiltrating)

Extrahepatic (eCCA)(i) Perihilar (Klatskin)
(ii) Distal
Mass-forming (nodular)
Periductal-infiltrating (sclerosing)
Intraductal (papillary)