Table 1: Characteristics of the adult CF cohort at the time of BPI-ANCA sampling (1995–1998).

Number of patients: ( )
 Total46
 Males26
 Females20
Age: (years)
 Mean26.2
 Range18.4–44.6
CFTR mutation: ( )
F508del/ F508del24
 Others22
FEV1.0 % predicted: ( )
 >80%16
 50–80%17
 <50%13
IgA BPI-ANCA:
 Negative ( 67 U)
  ( )17
  (mean age, years)27.5
 Positive (>67–200 U)
  ( )18
  (mean age, years)26.3
 High ( 200 U)
  ( )11
  (mean age, years)24.6
Leeds classification of PsA colonization: ( )
 I (chronic)24
 II (intermittent)2
 III (free of PsA)8
 IV (never PsA)12
Diabetes mellitus: ( )
 Yes5
 No34
 NA1