Table 3: Lung function, BPI-ANCA, and outcome. Patients divided into groups based lung function and IgA BPI-ANCA levels at baseline, and subsequent end-points during followup.

Lung functionFEV1 pred > 80% FEV1 pred 50–80% FEV1 pred < 50%
BPI-ANCA groupBPI−BPI+BPI++BPI−BPI+BPI++BPI−BPI+BPI++

Inclusion ( )11505**7*5166
5 years % with endpoint0020%14.3% 20%033%33%
( with endpoint)(1)(1*)(1)(2)(2)
10 years % with endpoint0040% 28.6% 40% 050%100%
( with endpoint)(2**)(2*)(2)(3)(6)
Last followup, % with endpoint0040% 42.8% 60% 100%66.7% 100%
( with endpoint)(2**)(3*)(3)(1)(4)(6)

Patient with colon cancer.
**Patient with Burkholderia cepacia.