Table 2: New classification of childhood vasculitis [2].

Predominantly large vessel vasculitisTakayasu arteritis

Predominantly medium-sized vessel vasculitisChildhood polyarteritis nodosa
Cutaneous polyarteritis
Kawasaki disease

Predominantly small vessels vasculitis(A) Granulomatous:
Wegener’s granulomatosis
Churg-Strauss syndrome
(B) Nongranulomatous:
Microscopic polyangiitis
Henoch-Schönlein purpura
Isolated cutaneous leucocytoclastic vasculitis
Hypocomplementic urticarial vasculitis

Other vasculitisBehcet disease
Vasculitis secondary to infection (including hepatitis B associated polyarteritis nodosa), malignancies, and drugs, including hypersensitivity vasculitis
Vasculitis associated with connective tissue diseases
Isolated vasculitis of the central nervous system
Cogan syndrome
Unclassified