Table 2: ANCA pattern recognition in sera containing BPI-ANCA or atypical ANCA.

Visual scoreAKLIDESConcordance

BPI-ANCA ( )9 C-ANCA6 negative, 3 ANA-dots0/9 (0.0%)
Atypical ANCA ( )8 negative, 9 C-ANCA,
5 atypical ANCA
18 negative, 2 C-ANCA, 1 P-ANCA,
1 undetermined
10/22 (45.5%)

ANA: antinuclear antibodies; ANCA: antineutrophil cytoplasmic antibodies; BPI: bactericidal permeability-increasing protein.