Research Article

Clinical Features and Genetic Analysis of 20 Chinese Patients with X-Linked Hyper-IgM Syndrome

Table 2

BCG vaccination-induced adverse drug reactions (ADR) and mycobacterium infections in XHIGM patients.

PatientsAgesPerformancesTreatments

P62 mBCGitis (ipsilateral axillary lymphadenitis)Surgery

P72 mBCGitis (ipsilateral axillary lymphadenitis)Surgery

P1250 dBCGitis (ipsilateral axillary lymphadenectasis)Antituberculosis medicine (rifampicin, unregularly)
35 mPulmonary tuberculosisAntituberculosis medicine (isoniazide + rifampicin + VitB6), antibiotics

P167 mBCGitis (ipsilateral axillary lymphadenitis)Surgery

P172 mBCGitis (ipsilateral axillary lymphadenitis)Surgery

P193 mBCGitis (ipsilateral cervical lymphadenectasis)Antituberculosis medicine

P148.5 yPulmonary tuberculosis, restrictive pulmonary capacity, splenomegaly and lymphadenopathyAntituberculosis medicine (isoniazide + rifampicin, unregularly), antibiotics, IVIG, thymosin
10 yTuberculous meningitisAntituberculosis medicine (isoniazide + rifampicin, unregularly)

Note: IVIG: intravenous immunoglobulin.