Research Article
Clinical Features and Genetic Analysis of 20 Chinese Patients with X-Linked Hyper-IgM Syndrome
Table 2
BCG vaccination-induced adverse drug reactions (ADR) and mycobacterium infections in XHIGM patients.
| Patients | Ages | Performances | Treatments |
| P6 | 2 m | BCGitis (ipsilateral axillary lymphadenitis) | Surgery |
| P7 | 2 m | BCGitis (ipsilateral axillary lymphadenitis) | Surgery |
|
P12 | 50 d | BCGitis (ipsilateral axillary lymphadenectasis) | Antituberculosis medicine (rifampicin, unregularly) | 35 m | Pulmonary tuberculosis | Antituberculosis medicine (isoniazide + rifampicin + VitB6), antibiotics |
| P16 | 7 m | BCGitis (ipsilateral axillary lymphadenitis) | Surgery |
| P17 | 2 m | BCGitis (ipsilateral axillary lymphadenitis) | Surgery |
| P19 | 3 m | BCGitis (ipsilateral cervical lymphadenectasis) | Antituberculosis medicine |
|
P14 | 8.5 y | Pulmonary tuberculosis, restrictive pulmonary capacity, splenomegaly and lymphadenopathy | Antituberculosis medicine (isoniazide + rifampicin, unregularly), antibiotics, IVIG, thymosin | 10 y | Tuberculous meningitis | Antituberculosis medicine (isoniazide + rifampicin, unregularly) |
|
|
Note: IVIG: intravenous immunoglobulin.
|