Research Article
Clinical Features and Genetic Analysis of 20 Chinese Patients with X-Linked Hyper-IgM Syndrome
Table 3
Laboratorial features in XHIGM patients.
| Patients () | IgG (g/L) | IgM (g/L) | IgA (g/L) | Lowest neutropenia (/L) | Absolute lymphocyte (/L) | Hb (g/L) | PLT (*1000/L) | CD3 (/L) | CD4 (/L) | CD8 (/L) | CD19 (/L) | CD4/CD8 | CD16/56 (/L) |
| P1 | <0.33 | 5.07 | <0.07 | 3780 | 2450 | 115 | 320 | NA | NA | NA | NA | NA | NA | P2 | 2.15 | 1.78 | 0.73 | 580 | 1498 | 90 | 479 | 1261 | 674 | 566 | 203 | 1.20 | 234 | P3 | 0.39 | 0.92 | 0.23 | 1390 | 2110 | 111 | 444 | 1139 | 635 | 433 | NA | 1.32 | NA | P4 | 0.08 | 9.48 | <0.22 | 26000 | 3600 | 83 | 679 | 1116 | 572 | 486 | 756 | 1.18 | 1152 | P5 | <0.33 | 2.73 | <0.07 | 900 | 3402 | 156 | 316 | 2007 | 700 | 1204 | 388 | 0.58 | 173 | P6 | <0.33 | 2 | <0.07 | 139 | 1470 | 100 | 293 | 1021 | 786 | 182 | 392 | 4.32 | 42 | P7 | 1.77 | 3.96 | <0.24 | 360 | 5364 | 126 | 175 | 4076 | 2789 | 1180 | 912 | 2.36 | 375 | P8 | 1.5 | 9.21 | 0.07 | 990 | 1285 | 100 | 184 | 1052 | 520 | 563 | 188 | 0.92 | 69 | P9 | <1.87 | 1.87 | <0.03 | 306 | 4618 | 59 | 311 | 4248 | 1662 | 2424 | 222 | 0.68 | 111 | P10 | 3.59 | 0.74 | 0.7 | 330 | 1350 | 81 | 243 | 999 | 729 | 189 | 346 | 3.86 | 28 | P11 | 1.81 | 4.1 | 0.35 | 2214 | 1140 | 68 | 92 | 949 | 307 | 485 | 144 | 0.63 | 40 | P12 | 0.32 | 3.65 | <0.07 | 377 | 6200 | 120 | 673 | 4625 | 2263 | 1761 | 1389 | 1.29 | 174 | P13 | 1.75 | 2.67 | <0.24 | 190 | 5600 | 117 | 143 | 4178 | 2610 | 1349 | 1277 | 1.93 | 140 | P14 | 2 | 3.56 | 0.52 | 200 | 1500 | 86 | 451 | 779 | 393 | 282 | 663 | 1.39 | 57 | P15 | 1.21 | 11.7 | 0.24 | 1800 | 2778 | 19 | 325 | 2000 | 909 | 949 | 541 | 0.96 | 225 | P16 | 0.45 | 2.24 | 0.55 | 2590 | 3360 | 117 | 335 | 2218 | 1277 | 605 | 706 | 2.14 | 370 | P17 | <0.33 | 1.98 | <0.07 | 2000 | 6300 | 108 | NA | 2553 | 1323 | 1017 | 3024 | 1.24 | 504 | P18 | 1.11 | 8.47 | 0.02 | 720 | 6140 | 112 | 476 | 4851 | 2579 | 1842 | 737 | 1.40 | 368 | P19 | 0.199 | 0.77 | <0.22 | 786 | 3144 | 96 | 633 | 2075 | 1100 | 1163 | 566 | 0.95 | 409 | P20 | 0.27 | 3.8 | 0.42 | 440 | 3188 | 98 | 656 | 2295 | 1243 | 638 | 542 | 1.95 | 223 |
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Note: NA: not available.
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