Heart Transplantation in Congenital Heart Disease: In Whom to Consider and When?
Figure 3
24 year old patient with heart failure and complex cardiac anatomy in the setting of left atrial isomerism. (a): Chest X-ray. (b): Axial slice of cardiac magnetic resonance imaging, showing a single atrium (SA) with direct connection of hepatic veins (arrow), dominant right ventricle (RV) and hypoplastic left ventricle (LV). (c): Coronal slice of cardiac magnetic resonance imaging showing hemiazygous continuation to left superior caval vein (arrows) in the absence of a right superior caval vein. (d): Apical echocardiographic view demonstrating the dominant right ventricle (RV), the hypoplastic left ventricle (LV), the enlarged single atrium (SA) and the dysplastic tricuspid valve. On the right hand of the panel color Doppler demonstrates severe tricuspid regurgitation.
