Research Article
Pulmonary Hypertension Related to Left-Sided Cardiac Pathology
Table 1
Classification system of pulmonary hypertension into groups 1–5 based on underlying disease process.
| Group 1 | Group 1′ | Group 2 | Group 3 | Group 4 | Group 5 |
| (i) Idiopathic (ii) Familial (iii) Connective tissue diseases (iv) Congenital shunt lesions (v) HIV (vi) Drugs/Toxins (vii) Hemoglobinopathies (viii) Portal hypertension (ix) Persistent pulmonary hypertension of the newborn | PVOD | (i) Left ventricular systolic/diastolic dysfunction (ii) Left-sided valvular dysfunction | Chronic lung diseases and/or hypoxemia | Chronic thromboembolic disease | Miscellaneous (i) Sarcoid (ii) Histiocytosis X (iii) Fibrosing mediastinitis (iv) Myeloproliferative disorders (v) Metabolic storage diseases (vi) Thyroid disease |
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