Guidelines

UK Guidelines for the Management of Bone Sarcomas

Table 1

2002 WHO classification of malignant bone tumours [16].

Osteogenic tumoursOsteosarcoma9180/3
Conventional9180/3
Chondroblastic9181/3
Fibroblastic9182/3
Osteoblastic9180/3
Telangiectatic9183/3
Small cell9185/3
Low-grade central9187/3
Secondary9180/3
Parosteal9192/3
Periosteal9193/3
High grade surface9194/3

Ewing sarcoma/primitive neuroectodermal tumourEwing sarcoma9260/3

CartilageChondrosarcoma9220/3
Central, primary, and secondary9220/3
Peripheral9221/3
Differentiated9243/3
Mesenchymal9240/3
Clear cell9242/3

Fibrogenic tumoursFibrosarcoma8810/3
Fibrohistiocytic tumours
Haemopoietic tumoursPlasma cell myeloma9732/3
Malignant lymphoma, NOS9590/3
Giant cell tumourMalignancy in giant cell tumour9250/3
Notochordal tumoursChordoma9370/3
Vascular tumoursAngiosarcoma9120/3
Smooth muscle tumoursLeiomyosarcoma8890/3
Lipogenic tumoursLiposarcoma8850/3
Miscellaneous tumoursAdamantinoma9261/3