Review Article
Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis
Table 2
Extracolonic FAP manifestation (Neiuwenhuis [
33] and Groen [
54]).
| Extracolonic manifestation | Prevalence in FAP patients |
| CHRPE | 70–75% | Osteomas and dental abnormalities | 70–90% | Upper GI tumors | 50–90% | Epidermoid cysts and lipomas | 25–50% | Desmoid tumors | 15–20% | Adrenal tumors | 7–13% | Papillary thyroid cancer | 1-2% | Hepatoblastoma | 1-2% | Brain Tumors (Medulloblastoma and others) | 1-2% | Pancreatic Cancer | 1% |
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