Histopathology of Pseudoxanthoma Elasticum and Related Disorders: Histological Hallmarks and Diagnostic Clues
Figure 6
Clinical features of the PXE-like disease with coagulation factor deficiency. Typical cutaneous peau d’orange lesions (a) may be the first sign. Natural history reveals an evolution towards thick redundant skin folds in the neck (b), the flexural regions and beyond (c).
